Search on: WOHLWILL-ANDRADE SYNDROME 
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Descriptor English:   Amyloid Neuropathies, Familial 
Descriptor Spanish:   neuropatías amiloideas familiares 
Descriptor Portuguese:   Neuropatias Amiloides Familiares 
Synonyms English:   Amyloid Neuropathy Type 1
Amyloid Neuropathy, Familial
Amyloid Polyneuropathies, Familial
Amyloid Polyneuropathy, British Type
Amyloid Polyneuropathy, Familial
Amyloid Polyneuropathy, Iowa Type
Amyloid Polyneuropathy, Swiss Type
Amyloid Syndrome, Neuropathic
Amyloid Syndromes, Neuropathic
Amyloidoses, Hereditary Neuropathic
Amyloidoses, Portuguese Polyneuritic
Amyloidosis, Hereditary Neuropathic
Amyloidosis, Portuguese Polyneuritic
Appalachian Type Familial Amyloid Polyneuropathy
British Type Amyloid Polyneuropathy
Cerebral Amyloid Angiopathy, British Type
Familial Amyloid Neuropathies
Familial Amyloid Neuropathy
Familial Amyloid Neuropathy, Andrade Type
Familial Amyloid Neuropathy, Finnish Type
Familial Amyloid Neuropathy, Portuguese Type
Familial Amyloid Polyneuropathies
Familial Amyloid Polyneuropathy
Familial Amyloid Polyneuropathy, Appalachian Type
Familial Amyloid Polyneuropathy, Jewish Type
Familial Amyloid Polyneuropathy, Type I
Familial Amyloid Polyneuropathy, Type II
Familial Amyloid Polyneuropathy, Type III
Familial Amyloid Polyneuropathy, Type IV
Familial Amyloid Polyneuropathy, Type V
Familial Amyloid Polyneuropathy, Type VI
Familial Portuguese Polyneuritic Amyloidosis
Finnish Type Familial Amyloid Neuropathy
Hereditary Neuropathic Amyloidoses
Hereditary Neuropathic Amyloidosis
Iowa Type Amyloid Polyneuropathy
Jewish Type Familial Amyloid Polyneuropathy
Neuropathic Amyloid Syndrome
Neuropathic Amyloid Syndromes
Neuropathic Amyloidoses, Hereditary
Neuropathic Amyloidosis, Hereditary
Neuropathies, Familial Amyloid
Neuropathy, Familial Amyloid
Polyneuritic Amyloidoses, Portuguese
Polyneuritic Amyloidosis, Portuguese
Polyneuropathies, Familial Amyloid
Polyneuropathy, Familial Amyloid
Portuguese Polyneuritic Amyloidoses
Portuguese Polyneuritic Amyloidosis
Portuguese Type Familial Amyloid Neuropathy
Swiss Type Amyloid Polyneuropathy
Type I Familial Amyloid Polyneuropathy
Type II Familial Amyloid Polyneuropathy
Type III Familial Amyloid Polyneuropathy
Type IV Familial Amyloid Polyneuropathy
Type V Familial Amyloid Polyneuropathy
Type VI Familial Amyloid Polyneuropathy
Wohlwill Andrade Syndrome
Wohlwill Corino Andrade Syndrome
Wohlwill-Andrade Syndrome
Wohlwill-Corino Andrade Syndrome  
Tree Number:   C10.574.500.050
C10.668.829.050.050
C16.320.400.050
C16.320.565.176.050
C18.452.648.176.050
C18.452.845.500.050.050
C18.452.845.500.075.050
Definition English:   Inherited disorders of the peripheral nervous system associated with the deposition of AMYLOID in nerve tissue. The different clinical types based on symptoms correspond to the presence of a variety of mutations in several different proteins including transthyretin (PREALBUMIN); APOLIPOPROTEIN A-I; and GELSOLIN. 
History Note English:   2002; use AMYLOID NEUROPATHIES 1994-2001; for FAMILIAL AMYLOID POLYNEUROPATHIES use AMYLOID NEUROPATHIES 1994-2001 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications DI diagnosis
DG diagnostic imaging DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RT radiotherapy
RH rehabilitation SU surgery
TH therapy UR urine
VE veterinary VI virology
Record Number:   36014 
Unique Identifier:   D028227 

Occurrence in VHL:
 

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